Amino acid disorders :
  ArgininosuccinicAciduna (ASA Lyase deficiency)
  Citrullinemia (ASA Synthetase deficiency)
  Homocystinuria (Cystathionine synthase def.)
  Maple Syrup Urine Disease (MSUD)
  Phenylketonuria (PKU)
  Tyrosinemia (Type I)
 

Fatty acid disorders :
  3-Hydroxy-3-methylglutaryl-CoA lyase def. (3HMG)
  Long chain Hydroxy Acyl-CoA Dehydrogenase def. (LCHAD)
  Medium Chain Acyl-CoA Dehydrogenase def. (MCAD)

  Trifunctional protein deficiency (TFP)
  Very Long Chain Acyl-CoA dehydrogenase def. (VLCAD)

Organic acid disorders :
  3-Methylcrotonyl-CoA Carboxylase def. (3MCC)
  Beta Ketothiolase deficiency (Mitochondral Acetoacetyl CoA Thiolase def)
  Glutaric Acidemia Type I (GA-I))
  Isovaleric Acidemia (IVA)
  Methyl Malonic Acidemia (MMA)
  Multiple CoA Carboxylase def. (MCD)
  Propionic Acidemia (PA)